Standard knownness: 1.7; Custom knownness: None; Num. species: 39; Orthology database: Panther19.0; Protein members: 42
Molecular function: cobalamin metabolic process2016, 2021, 2024
Cellular component: mitochondrion2016, 2018, 2020, 2024 cytoplasm2016, 2024 cytosol2013, 2021, 2024
| Chordates: | 22/21 | ![]()  | 
                   
                 
| Echinoderms: | 0/0 | |
| Hemichordates: | 1/1 | |
| Annelids: | 1/1 | |
| Molluscs: | 0/0 | |
| Bryozoans: | 0/0 | |
| Platyhelminthes: | 0/0 | |
| Rotifers: | 0/0 | |
| Nematodes: | 3/3 | |
| Arthropods: | 4/5 | |
| Tardigrades: | 0/0 | |
| Placozoa: | 1/1 | |
| Cnidaria: | 1/1 | |
| Porifera: | 0/0 | |
| Choanoflagellates+: | 0/1 | |
| Dikarya: | 0/14 | |
| Fungi (other): | 0/1 | |
| Protozoa: | 2/3 | |
| Excavates: | 0/4 | |
| Harosa: | 1/4 | |
| Hacrobia: | 0/0 | |
| Plants: | 2/39 | |
| Archea: | 0/8 | |
| Bacteria: | 1/35 | 
Click here to switch to the previous version of the database.
| UniProt ID Organism DB»  | 
	    
        
          
            Standard knownness | clustom knownness | Gene name | Description | Species [Key only] | GO terms | Seq. links | Protein domain links | |||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 
        A0A1Y1IDR6_KLENI EnsemblPlants»  | 
        
          
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        KFL_004540080 | Methylmalonic aciduria and homocystinuria type D protein  | 
        
        Klebsormidium nitens TI:105231 None  | 
        
          
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        A0A2I2Y5E5_GORGO Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D | 
        Gorilla gorilla TI:9593 None  | 
        
          
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| 
        A0A2I3TEW6_PANTR Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D | 
        Pan troglodytes TI:9598 None  | 
        
          
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| 
        A0A2K3DY98_CHLRE EnsemblPlants»  | 
        
          
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        CHLRE_03g189200v5 | Methylmalonic aciduria and homocystinuria type D protein  | 
        
        Chlamydomonas reinhardtii TI:3055 None  | 
        
          
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| 
        A0A3Q1M6Z9_BOVIN Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D | 
        Bos taurus TI:9913 None  | 
        
          
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| 
        A0A7M7P8F5_STRPU EnsemblMetazoa»  | 
        
          
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        Uncharacterized protein | 
        Strongylocentrotus purpuratus TI:7668 None  | 
        
          
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| 
        A0A803T8J2_ANOCA Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D | 
        Anolis carolinensis TI:28377 None  | 
        
          
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| 
        A0A8I3N3R1_CANLF Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D | 
        Canis lupus TI:9612 None  | 
        
          
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| 
        A0A8R1V1I6_PRIPA EnsemblMetazoa»  | 
        
          
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        WBGene00284261 | Uncharacterized protein | 
        Pristionchus pacificus TI:54126 None  | 
        
          
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| 
        A7RUY2_NEMVE EnsemblMetazoa»  | 
        
          
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        NEMVEDRAFT_v1g94190 | Methylmalonic aciduria and homocystinuria type D homolog, mitochondrial-like  | 
        
        Nematostella vectensis TI:45351 None  | 
        
          
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| 
        A8XLX1_CAEBR WormBase»  | 
        
          
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        CBG15313 CBG_15313 | Protein CBG15313 | 
        Caenorhabditis briggsae TI:6238 None  | 
        
          
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| 
        B0UYB6_DANRE ZFIN»  | 
        
          
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        My011 | Metabolism of cobalamin associated D (Methylmalonic aciduria and homocystinuria type D protein, mitochondrial)  | 
        
        Danio rerio TI:7955 None  | 
        
          
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| 
        B3RQY7_TRIAD EnsemblMetazoa»  | 
        
          
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        TRIADDRAFT_22771 | Methylmalonic aciduria and homocystinuria type D protein, mitochondrial  | 
        
        Trichoplax adhaerens TI:10228 None  | 
        
          
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| 
        B7PW32_IXOSC EnsemblMetazoa»  | 
        
          
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        IscW_ISCW024444 | Uncharacterized protein | 
        Ixodes scapularis TI:6945 None  | 
        
          
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| 
        C3YW38_BRAFL CTD»  | 
        
          
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        LOC118423745 | Cobalamin trafficking protein CblD-like | 
        Branchiostoma floridae TI:7739 None  | 
        
          
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| 
        D6W9C4_TRICA EnsemblMetazoa»  | 
        
          
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        AUGUSTUS-3.0.2_00972 | Methylmalonic aciduria and homocystinuria type D homolog, mitochondrial-like Protein  | 
        
        Tribolium castaneum TI:7070 None  | 
        
          
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| 
        E1JHJ7_DROME FlyBase»  | 
        
          
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        CG15133 | FI21943p1 | 
        Drosophila melanogaster TI:7227 None  | 
        
          
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| 
        E9FQQ4_DAPPU EnsemblMetazoa»  | 
        
          
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        DAPPUDRAFT_190063 | Methylmalonic aciduria and homocystinuria type D protein, mitochondrial  | 
        
        Daphnia pulex TI:6669 None  | 
        
          
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| 
        F1A4M1_DICPU EnsemblProtists»  | 
        
          
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        DICPUDRAFT_43706 | Methylmalonic aciduria and homocystinuria type D protein  | 
        
        Dictyostelium purpureum TI:5786 None  | 
        
          
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| 
        F6WCH6_MACMU Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D (Methylmalonic aciduria and homocystinuria type D protein, mitochondrial)  | 
        
        Macaca mulatta TI:9544 None  | 
        
          
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| 
        F6WS42_CIOIN Ensembl»  | 
        
          
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        Methylmalonic aciduria and homocystinuria type D protein, mitochondrial  | 
        
        Ciona intestinalis TI:7719 None  | 
        
          
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| 
        F7DJV3_HORSE Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D | 
        Equus caballus TI:9796 None  | 
        
          
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| 
        F7G126_MONDO Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D | 
        Monodelphis domestica TI:13616 None  | 
        
          
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| 
        H2LH66_ORYLA Ensembl»  | 
        
          
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        mmadhc | Metabolism of cobalamin associated D | 
        Oryzias latipes TI:8090 None  | 
        
          
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| 
        H3GEE8_PHYRM EnsemblProtists»  | 
        
          
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        Methylmalonic aciduria and homocystinuria type D protein  | 
        
        Phytophthora ramorum TI:164328 None  | 
        
          
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| 
        I3LE45_PIG Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D (Methylmalonic aciduria and homocystinuria type D protein, mitochondrial)  | 
        
        Sus scrofa TI:9823 None  | 
        
          
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| 
        K7EDL1_ORNAN Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D | 
        Ornithorhynchus anatinus TI:9258 None  | 
        
          
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| 
        M3W3N6_FELCA Ensembl»  | 
        
          
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        MMADHC | Metabolism of cobalamin associated D | 
        Felis catus TI:9685 None  | 
        
          
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| 
        MMAD_CHICK Ensembl»  | 
        
          
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        MMADHC | Cobalamin trafficking protein CblD (CblD) (Methylmalonic aciduria and homocystinuria type D homolog, mitochondrial)  | 
        
        Gallus gallus TI:9031 None  | 
        
          
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| 
        MMAD_HUMAN Ensembl»  | 
        
          
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        MMADHC | Cobalamin trafficking protein CblD (CblD) (Methylmalonic aciduria and homocystinuria type D protein, mitochondrial)  | 
        
        Homo sapiens TI:9606 None  | 
        
          
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| 
        MMAD_MOUSE Ensembl»  | 
        
          
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        Mmadhc | Cobalamin trafficking protein CblD (CblD) (Methylmalonic aciduria and homocystinuria type D homolog, mitochondrial)  | 
        
        Mus musculus TI:10090 None  | 
        
          
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| 
        MMAD_RAT RGD»  | 
        
          
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        Mmadhc | Cobalamin trafficking protein CblD (CblD) (Methylmalonic aciduria and homocystinuria type D homolog, mitochondrial)  | 
        
        Rattus norvegicus TI:10116 None  | 
        
          
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| 
        Q28J68_XENTR Xenbase»  | 
        
          
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        mmadhc | Methylmalonic aciduria and homocystinuria type D protein, mitochondrial (Methylmalonic aciduria and homocystinuria type D protein, mitochondrial isoform X1) (Novel protein)  | 
        
        Xenopus tropicalis TI:8364 None  | 
        
          
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| 
        Q4V7U5_XENLA Xenbase»  | 
        
          
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        mmadhc.L | MGC115384 protein (Metabolism of cobalamin associated D L homeolog)  | 
        
        Xenopus laevis TI:8355 None  | 
        
          
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| 
        Q54QF8_DICDI dictyBase»  | 
        
          
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        DDB_G0283849 | Uncharacterized protein | 
        Dictyostelium discoideum TI:44689 None  | 
        
          
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        |||||
| 
        Q58E85_XENLA Xenbase»  | 
        
          
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        mmadhc.S | MGC84965 protein (Uncharacterized protein LOC735071)  | 
        
        Xenopus laevis TI:8355 None  | 
        
          
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| 
        Q6DHF6_DANRE ZFIN»  | 
        
          
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        mmadhca | Methylmalonic aciduria (Cobalamin deficiency) cblD type, with homocystinuria (Methylmalonic aciduria (Cobalamin deficiency) cblD type, with homocystinuria isoform X1) (Zgc:92335)  | 
        
        Danio rerio TI:7955 None  | 
        
          
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| 
        Q7NK41_GLOVI EnsemblBacteria»  | 
        
          
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        glr1639 | Glr1639 protein | 
        Gloeobacter violaceus TI:33072 None  | 
        
          
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| 
        Q9W375_DROME FlyBase»  | 
        
          
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  | 
        Dmel\CG12118 | LP04941p (Uncharacterized protein, isoform A) (Uncharacterized protein, isoform B)  | 
        
        Drosophila melanogaster TI:7227 None  | 
        
          
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| 
        Q9XWC9_CAEEL WormBase»  | 
        
          
  | 
        
          
  | 
        CELE_Y76A2B.5 Y76A2B.5 | Methylmalonic aciduria and homocystinuria type D protein, mitochondrial  | 
        
        Caenorhabditis elegans TI:6239 None  | 
        
          
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| 
        T1FXD6_HELRO EnsemblMetazoa»  | 
        
          
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  | 
        20213484 | Methylmalonic aciduria and homocystinuria type D protein, mitochondrial  | 
        
        Helobdella robusta TI:6412 None  | 
        
          
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| 
        W5M078_LEPOC Ensembl»  | 
        
          
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        Metabolism of cobalamin associated D | 
        Lepisosteus oculatus TI:7918 None  | 
        
          
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